In March 1996, the British Parliament announced that there is a probable link between vCJD and BSE. They start to act very bizarrely, lose control of their bodily functions, and eventually die. (Photo by Liaison) Here's a look at Mad Cow Disease, a fatal brain disease found in cattle. CJD is an extremely rare and deeply unusual disease that affects the brain, causing symptoms such as depression, memory problems, behavioral changes, poor … Symptoms include abnormal behavior, trouble walking, and weight loss. Fish & Wildlife Service. What is Mad Cow Disease (Bovine Spongiform Encephalopathy or BSE)? Multiple System Atrophy, a brain disorder,is caused by anewly-discovered prion linking it to incurable diseases like mad cow andCreutzfeldt-Jakob disease, according to new research. CWD (Chronic Wasting Disease) CWD is a prion disease that affects deer, elk and moose in some areas of North America, South Korea and Norway. The illness makes deer act like zombies. The disease creates holes in the brain tissue so that the brain resembles a sponge, and nerve cells in the brain are lost. A spinal fluid test is performed to see the presence of protein similar to mad cow disease in the spinal fluid. Mad cow, meet mad deer State authorities are planning to kill 15,000 deer in the hills of southwest Wisconsin. This is the deer equivalent of “mad cow disease." The reason? Also like mad cow disease, in its early days at least, some scientists have scoffed at the notion it can be transmitted to humans. BSE is a neurologic disease that affects the brain structure of infected cattle, according to the USDA. Variant CJD is linked to an epidemic of bovine spongiform encephalopathy (BSE) or ‘mad cow disease’, as it is known in the media. EEG can be done to examine the brain waves Mad cow disease is a rare illness and is therefore not diagnosed easily by the doctor. Those cases were linked to food contaminated with bovine spongiform encephalopathy (BSE), a prion disease that causes variant CJD, otherwise known as "mad cow" disease. These deer may look innocent, but they may carry a dangerous brain disease. Early symptoms include memory problems, behavioral changes, poor coordination, and visual disturbances. ... Elk and deer hunters in Colorado and Wyoming have been alerted to a fatal brain disease found in the big game similar to mad cow disease, but officials said no evidence exists the disease is transmitted to humans. Like another disease that is spread among brain-eating cannibals in New Guinea called kuru, Creuzfeldt-Jakob disease causes progressive loss of brain functions that slowly destroy mobility and personality and inevitably result in death over a period of 6 to 24 months. Onset of familial CJD occurs slightly earlier and vCJD has affected people at a much younger age, usually in their late 20s. Clumps of rogue proteins are not the cause of fatal conditions such as mad cow disease, but merely a symptom, hints new research. WASHINTGON (CBSDC) — A rare and incurable brain disease is caused by a misfolded brain protein similar to the one that causes mad cow disease, according to … Like mad cow disease, CWD attacks the brain and spinal cord and is believed to be caused by prions, infectious proteins that travel in bodily fluids and remain contagious for years after leaving the body of their host. U.S. Prions are insidious proteins that spread like infectious agents and trigger fatal conditions such as mad cow disease. Infected cows act “mad… That is, it moves through the spinal cord and brain, literally killing brain cells and leaving holes in the brain.The visible effects of this disease are erratic, or insane, behavior in the infected cow, hence the name mad cow disease. 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